Elevated growth differentiation factor 15 expression in patients with congenital dyserythropoietic anemia type I.

نویسندگان

  • Hannah Tamary
  • Hanna Shalev
  • Galit Perez-Avraham
  • Meira Zoldan
  • Itai Levi
  • Dorine W Swinkels
  • Toshihiko Tanno
  • Jeffery L Miller
چکیده

Congenital dyserythropoietic anemia (CDA) is a rare group of red blood cell disorders characterized by ineffective erythropoiesis and increased iron absorption. To determine whether growth differentation factor 15 (GDF15) hyper-expression is associated with the ineffective erythropoiesis and iron-loading complications of CDA type I (CDA I), GDF15 levels and other markers of erythropoiesis and iron overload were studied in blood from 17 CDA I patients. Significantly higher levels of GDF15 were detected among the CDA I patients (10 239 +/- 3049 pg/mL) compared with healthy volunteers (269 +/- 238 pg/mL). In addition, GDF15 correlated significantly with several erythropoietic and iron parameters including Hepcidin-25, Ferritin, and Hepcidin-25/Ferritin ratios. These novel results suggest that CDA I patients express very high levels of serum GDF15, and that GDF15 contributes to the inappropriate suppression of hepcidin with subsequent secondary hemochromatosis.

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عنوان ژورنال:
  • Blood

دوره 112 13  شماره 

صفحات  -

تاریخ انتشار 2008